Our report indicates that the Fontan operation is very effective for ARVD and should be considered in the treatment of such patients, particularly those with refractory tachycardia. Concerning postoperative management, massive vasodilatory therapy and early extubation should be used to reduce pulmonary vascular resistance as much as possible, as in the Fontan operation in patients with congenital heart disease.
- Arrhythmogenic right ventricular dysplasia
- Fontan operation
- Pulmonary vascular resistance
ASJC Scopus subject areas
- Anesthesiology and Pain Medicine