Abstract
A 41-year-old man was diagnosed with immunoglobulin G4-related disease (IgG4-RD) in both eyelids 4 years ago and exhibited good response to steroid therapy. However, rapid swelling of the right eyelid lesion was recently observed. As IgG4-RD progression was suspected, biopsy was performed. Although the histology was consistent with IgG4-RD, the infiltrating large atypical lymphoid cells showed immunoglobulin light-chain restriction and IgH gene rearrangement. Consequently, he was diagnosed with extranodal marginal zone lymphoma with abundant IgG4-positive cells.
Original language | English |
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Pages (from-to) | 383-387 |
Number of pages | 5 |
Journal | Modern Rheumatology |
Volume | 29 |
Issue number | 2 |
DOIs | |
Publication status | Published - Mar 4 2019 |
Keywords
- IgG4-related disease
- marginal zone lymphoma
- ocular adnexa
ASJC Scopus subject areas
- Rheumatology