Neuromyelitis Optica Spectrum Disorder Coinciding with Spinocerebellar Ataxia Type 31

Yoshiaki Takahashi, Yasuhiro Manabe, Ryuta Morihara, Hisashi Narai, Toru Yamashita, Koji Abe

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

We report the unusual case of a 63-year-old man with spinocerebellar ataxia (SCA) type 31 who developed neuromyelitis optica spectrum disorder (NMOSD) 14 years after the onset of cerebellar symptoms. In addition to cerebellar atrophy, magnetic resonance imaging showed multiple high-intensity areas in the brain and a long thoracic cord lesion from Th1/2 to Th11. The combination of NMOSD and SCA31 is accidental. However, our case suggests that inflammatory processes could be involved in the pathogenesis of NMOSD and SCA31.

Original languageEnglish
Pages (from-to)127-130
Number of pages4
JournalCase Reports in Neurology
DOIs
Publication statusAccepted/In press - May 17 2017

Fingerprint

Neuromyelitis Optica
Atrophy
Spinal Cord
Magnetic Resonance Imaging
Brain
Spinocerebellar Ataxia 31

Keywords

  • Anti-aquaporin-4 antibody
  • Autoimmune disease
  • Central nervous system disease
  • Neurodegeneration
  • Neuromyelitis optica spectrum disorder
  • Spinocerebellar ataxia type 31

ASJC Scopus subject areas

  • Clinical Neurology

Cite this

Neuromyelitis Optica Spectrum Disorder Coinciding with Spinocerebellar Ataxia Type 31. / Takahashi, Yoshiaki; Manabe, Yasuhiro; Morihara, Ryuta; Narai, Hisashi; Yamashita, Toru; Abe, Koji.

In: Case Reports in Neurology, 17.05.2017, p. 127-130.

Research output: Contribution to journalArticle

Takahashi, Yoshiaki ; Manabe, Yasuhiro ; Morihara, Ryuta ; Narai, Hisashi ; Yamashita, Toru ; Abe, Koji. / Neuromyelitis Optica Spectrum Disorder Coinciding with Spinocerebellar Ataxia Type 31. In: Case Reports in Neurology. 2017 ; pp. 127-130.
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