Mediastinal extracardiac fetal rhabdomyoma; Case report

Go Miyano, Hiromu Miyake, Masakatsu Kaneshiro, Keiichi Morita, Hiroshi Nouso, Masaya Yamoto, Koji Fukumoto, Yasuo Horikoshi, Kazuko Kudo, Minoru Hamazaki, Naoto Urushihara

Research output: Contribution to journalArticle

Abstract

A 9-month-old girl with a small suprasternal mass was referred for treatment after fine needle aspiration of the mass elsewhere suggested rhabdomyosarcoma. On admission, magnetic resonance imaging (MRI) identified a 58 × 42 mm oval mass in the anterior mediastinum close to the common carotid artery and aortic arch. Surgical intervention was initially considered to be too risky, but after a trial of chemotherapy failed to reduce the size of the tumor, complete local excision was planned through a vertical median thoracic incision with median sternotomy. Surgery was performed when she was 10 months old. Due to severe adhesions, the left clavicle, first rib and the sternoclavicular joint needed to be partially resected to allow the tumor to be completely excised with safety. Operating time was 3 h; intraoperative blood loss was 123 mL requiring intraoperative transfusion. Histopathology and immunohistochemistry were consistent with an intermediate form of fetal rhabdomyoma. The postoperative course was uneventful and she is currently alive with no evidence of disease 4 years later. Fetal rhabdomyoma is rare and our case presented with a small, asymptomatic, suprasternal mass. While the distinction between rhabdomyoma and rhabdomyosarcoma can be difficult, a multidisciplinary approach enabled surgery to be performed successfully.

Original languageEnglish
Pages (from-to)196-199
Number of pages4
JournalJournal of Pediatric Surgery Case Reports
Volume2
Issue number4
DOIs
Publication statusPublished - Apr 2014
Externally publishedYes

Keywords

  • Median sternotomy
  • Mediastinal
  • Rhabdomyoma

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Surgery

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  • Cite this

    Miyano, G., Miyake, H., Kaneshiro, M., Morita, K., Nouso, H., Yamoto, M., Fukumoto, K., Horikoshi, Y., Kudo, K., Hamazaki, M., & Urushihara, N. (2014). Mediastinal extracardiac fetal rhabdomyoma; Case report. Journal of Pediatric Surgery Case Reports, 2(4), 196-199. https://doi.org/10.1016/j.epsc.2014.03.015