A long-term follow-up study of vestibuloauditory symptoms was presented in a patient with Cogan's syndrome. The patient was a 45-years-old female developing bilateral fluctuant but progressive hearing loss associated with ocular symptoms and fever of unknown origin. Neuro-otological examination revealed bilateral sensorineural hearing loss of cochlear type and vestibular dysfunction of peripheral type. Cogan's syndrome was suspected clinically and a systemic administration of steroids was started. Hearing loss of the right ear was significantly improved at low and middle frequencies with decreased incidence of vertigo. The auditory and vestibular functions maintain the improved levels for nearly three years by persistent systemic administration of peroral corticosteroids.
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