Abstract
Left ventricular (LV) retraining followed by anatomical repair would be a superior alternative in patients with congenitally corrected transposition (ccTGA) having a deconditioned morphologically left ventricle (MLV); however, LV retraining in older children is a challenging task. A retraining process of the MLV in a teenage patient with ccTGA is reported here. Cardiac catheterization at 7 years of age revealed low pressure of the MLV (33/4 mm Hg) and a LV to right ventricular pressure ratio (LVp/RVp ratio) of 0.32. The first pulmonary artery banding (PAB) was performed at 10 years of age. Although the LVp/RVp ratio reached 0.68, there was no evidence of adequate LV hypertrophy. The second PAB was performed 2 years after the initial PAB, resulting in an increase in the LVp/RVp ratio to 0.93 and an adequate LV hypertrophy. The double switch procedure was successfully performed at 13 years of age. Although the ejection fraction of the MLV mildly decreased, the patient has been doing well during a follow-up period of 4 years. The MLV in the teenage patient with ccTGA was successfully trained using a retraining strategy and has sustained systemic circulation after anatomical repair.
| Original language | English |
|---|---|
| Pages (from-to) | 613-616 |
| Number of pages | 4 |
| Journal | Circulation Journal |
| Volume | 71 |
| Issue number | 4 |
| DOIs | |
| Publication status | Published - 2007 |
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Keywords
- Congenitally corrected transposition of the great arteries
- Double switch operation
- Left ventricular retraining
ASJC Scopus subject areas
- Cardiology and Cardiovascular Medicine
- Physiology
Cite this
Left ventricular retraining and anatomic correction in teenage patient with congenitally corrected transposition of the great arteries. / Honjo, Osami; Kawada, Masaaki; Akagi, Teiji; Kotani, Yasuhiro; Ishino, Kozo; Sano, Shunji.
In: Circulation Journal, Vol. 71, No. 4, 2007, p. 613-616.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Left ventricular retraining and anatomic correction in teenage patient with congenitally corrected transposition of the great arteries
AU - Honjo, Osami
AU - Kawada, Masaaki
AU - Akagi, Teiji
AU - Kotani, Yasuhiro
AU - Ishino, Kozo
AU - Sano, Shunji
PY - 2007
Y1 - 2007
N2 - Left ventricular (LV) retraining followed by anatomical repair would be a superior alternative in patients with congenitally corrected transposition (ccTGA) having a deconditioned morphologically left ventricle (MLV); however, LV retraining in older children is a challenging task. A retraining process of the MLV in a teenage patient with ccTGA is reported here. Cardiac catheterization at 7 years of age revealed low pressure of the MLV (33/4 mm Hg) and a LV to right ventricular pressure ratio (LVp/RVp ratio) of 0.32. The first pulmonary artery banding (PAB) was performed at 10 years of age. Although the LVp/RVp ratio reached 0.68, there was no evidence of adequate LV hypertrophy. The second PAB was performed 2 years after the initial PAB, resulting in an increase in the LVp/RVp ratio to 0.93 and an adequate LV hypertrophy. The double switch procedure was successfully performed at 13 years of age. Although the ejection fraction of the MLV mildly decreased, the patient has been doing well during a follow-up period of 4 years. The MLV in the teenage patient with ccTGA was successfully trained using a retraining strategy and has sustained systemic circulation after anatomical repair.
AB - Left ventricular (LV) retraining followed by anatomical repair would be a superior alternative in patients with congenitally corrected transposition (ccTGA) having a deconditioned morphologically left ventricle (MLV); however, LV retraining in older children is a challenging task. A retraining process of the MLV in a teenage patient with ccTGA is reported here. Cardiac catheterization at 7 years of age revealed low pressure of the MLV (33/4 mm Hg) and a LV to right ventricular pressure ratio (LVp/RVp ratio) of 0.32. The first pulmonary artery banding (PAB) was performed at 10 years of age. Although the LVp/RVp ratio reached 0.68, there was no evidence of adequate LV hypertrophy. The second PAB was performed 2 years after the initial PAB, resulting in an increase in the LVp/RVp ratio to 0.93 and an adequate LV hypertrophy. The double switch procedure was successfully performed at 13 years of age. Although the ejection fraction of the MLV mildly decreased, the patient has been doing well during a follow-up period of 4 years. The MLV in the teenage patient with ccTGA was successfully trained using a retraining strategy and has sustained systemic circulation after anatomical repair.
KW - Congenitally corrected transposition of the great arteries
KW - Double switch operation
KW - Left ventricular retraining
UR - http://www.scopus.com/inward/record.url?scp=34047136512&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=34047136512&partnerID=8YFLogxK
U2 - 10.1253/circj.71.613
DO - 10.1253/circj.71.613
M3 - Article
C2 - 17384468
AN - SCOPUS:34047136512
VL - 71
SP - 613
EP - 616
JO - Circulation Journal
JF - Circulation Journal
SN - 1346-9843
IS - 4
ER -