TY - JOUR
T1 - Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome
AU - Sugiyama, Hirotaro
AU - Tachibana, Motomi
AU - Morita, Hiroshi
AU - Nishii, Nobuhiro
AU - Miyoshi, Akihito
AU - Sugiyama, Hiroyasu
AU - Nakagawa, Koji
AU - Watanabe, Atsuyuki
AU - Nakamura, Kazufumi
AU - Ito, Hiroshi
N1 - Publisher Copyright:
© 2016 Japanese Heart Rhythm Society
Copyright:
Copyright 2017 Elsevier B.V., All rights reserved.
PY - 2017/6
Y1 - 2017/6
N2 - A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.
AB - A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.
KW - Congenital long QT syndrome
KW - Implantable cardioverter-defibrillator
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U2 - 10.1016/j.joa.2016.10.561
DO - 10.1016/j.joa.2016.10.561
M3 - Article
AN - SCOPUS:85006124072
VL - 33
SP - 237
EP - 239
JO - Journal of Arrhythmia
JF - Journal of Arrhythmia
SN - 1880-4276
IS - 3
ER -