Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome

Hirotaro Sugiyama; Motomi Tachibana; Hiroshi Morita; Nobuhiro Nishii; Akihito Miyoshi; Hiroyasu Sugiyama; Koji Nakagawa; Atsuyuki Watanabe; Kazufumi Nakamura; Hiroshi Ito

doi:10.1016/j.joa.2016.10.561

Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome

Hirotaro Sugiyama, Motomi Tachibana, Hiroshi Morita, Nobuhiro Nishii, Akihito Miyoshi, Hiroyasu Sugiyama, Koji Nakagawa, Atsuyuki Watanabe, Kazufumi Nakamura, Hiroshi Ito

Research output: Contribution to journal › Article › peer-review

3 Citations (Scopus)

Abstract

A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.

Original language	English
Pages (from-to)	237-239
Number of pages	3
Journal	journal of arrhythmia
Volume	33
Issue number	3
DOIs	https://doi.org/10.1016/j.joa.2016.10.561
Publication status	Published - Jun 2017

Keywords

Congenital long QT syndrome
Implantable cardioverter-defibrillator

ASJC Scopus subject areas

Cardiology and Cardiovascular Medicine

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10.1016/j.joa.2016.10.561

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title = "Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome",

abstract = "A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.",

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doi = "10.1016/j.joa.2016.10.561",

language = "English",

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AU - Sugiyama, Hirotaro

AU - Tachibana, Motomi

AU - Morita, Hiroshi

AU - Nishii, Nobuhiro

AU - Miyoshi, Akihito

AU - Sugiyama, Hiroyasu

AU - Nakagawa, Koji

AU - Watanabe, Atsuyuki

AU - Nakamura, Kazufumi

AU - Ito, Hiroshi

PY - 2017/6

Y1 - 2017/6

N2 - A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.

AB - A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.

KW - Congenital long QT syndrome

KW - Implantable cardioverter-defibrillator

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Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome

Abstract

Keywords

ASJC Scopus subject areas

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