Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome

Hirotaro Sugiyama; Motomi Tachibana; Hiroshi Morita; Nobuhiro Nishii; Akihito Miyoshi; Hiroyasu Sugiyama; Koji Nakagawa; Atsuyuki Watanabe; Kazufumi Nakamura; Hiroshi Ito

doi:10.1016/j.joa.2016.10.561

Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome

Hirotaro Sugiyama, Motomi Tachibana, Hiroshi Morita, Nobuhiro Nishii, Akihito Miyoshi, Hiroyasu Sugiyama, Koji Nakagawa, Atsuyuki Watanabe, Kazufumi Nakamura, Hiroshi Ito

Research output: Contribution to journal › Article

3 Citations (Scopus)

Abstract

A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.

Original language	English
Journal	Journal of Arrhythmia
DOIs	https://doi.org/10.1016/j.joa.2016.10.561
Publication status	Accepted/In press - Sep 17 2016

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Keywords

Congenital long QT syndrome
Implantable cardioverter-defibrillator

ASJC Scopus subject areas

Cardiology and Cardiovascular Medicine

Cite this

Sugiyama, H., Tachibana, M., Morita, H., Nishii, N., Miyoshi, A., Sugiyama, H., Nakagawa, K., Watanabe, A., Nakamura, K., & Ito, H. (Accepted/In press). Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome. Journal of Arrhythmia. https://doi.org/10.1016/j.joa.2016.10.561

Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome. / Sugiyama, Hirotaro; Tachibana, Motomi; Morita, Hiroshi ; Nishii, Nobuhiro ; Miyoshi, Akihito; Sugiyama, Hiroyasu; Nakagawa, Koji ; Watanabe, Atsuyuki ; Nakamura, Kazufumi ; Ito, Hiroshi.

In: Journal of Arrhythmia, 17.09.2016.

Research output: Contribution to journal › Article

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AU - Miyoshi, Akihito

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AU - Nakagawa, Koji

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AB - A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.

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Access to Document

10.1016/j.joa.2016.10.561