Dravet syndrome with an exceptionally good seizure outcome in two adolescents

Katsuhiro Kobayashi; Iori Ohmori; Mamoru Oouchida; Yoko Ohtsuka

doi:10.1684/epd.2011.0453

Dravet syndrome with an exceptionally good seizure outcome in two adolescents

Katsuhiro Kobayashi, Iori Ohmori, Mamoru Oouchida, Yoko Ohtsuka

Research output: Contribution to journal › Article

3 Citations (Scopus)

Abstract

We present two children who exhibited the characteristics of Dravet syndrome during infancy and young childhood, with SCN1A mutation, but nevertheless achieved seizure freedom for at least four years during adolescence. These patients had no episodes of convulsive status epilepticus with a duration of more than 30 minutes and their overall favourable seizure outcome may be related to the prevention of convulsive status epilepticus.

Original language	English
Pages (from-to)	340-344
Number of pages	5
Journal	Epileptic Disorders
Volume	13
Issue number	3
DOIs	https://doi.org/10.1684/epd.2011.0453
Publication status	Published - Sep 2011

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Keywords

Adolescence
Convulsive status epilepticus
Dravet syndrome
Prognosis
SCN1A mutation
Severe myoclonic epilepsy in infancy

ASJC Scopus subject areas

Clinical Neurology
Neurology

Cite this

Kobayashi, K., Ohmori, I., Oouchida, M., & Ohtsuka, Y. (2011). Dravet syndrome with an exceptionally good seizure outcome in two adolescents. Epileptic Disorders, 13(3), 340-344. https://doi.org/10.1684/epd.2011.0453

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Access to Document

10.1684/epd.2011.0453