Recently, the effectiveness of cochlear implantation for hereditary deafness has been reported. We performed cochlear implantation for two patients with symptomatic hereditary deafness. Deafness in one patient was thought to be a result of albinism-deafness syndrome and in the other patient, a result of chronic progressive external ophthalmoplegia syndrome. Since their speech perception abilities improved dramatically, we believe that cochlear implantation should be actively performed for these two syndromes.
|Number of pages||4|
|Journal||Acta Oto-Laryngologica, Supplement|
|Publication status||Published - Jul 28 1999|
- Albinism-deafness syndrome
- Chronic progressive external ophthalmoplegia syndrome
- Cochlear implantation
ASJC Scopus subject areas