Clinical findings on ANCA-associated renal vasculitis from the Japan RPGN registry obtained via a questionnaire survey

Kunihiro Yamagata, Joichi Usui, Hitoshi Sugiyama, Kosaku Nitta, Takashi Wada, Eri Muso, Yoshihiro Arimura, Akio Koyama, Hirofumi Makino, Seiichi Matsuo

Research output: Contribution to journalReview article

5 Citations (Scopus)

Abstract

Renal involvement with significant organ damage is common in anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV). As a result, it is independently referred to ANCA-associated renal vasculitis. Clinically, ANCA-associated renal vasculitis is characterized by rapidly progressive glomerulonephritis. Pathologically, it is defined by pauci-immune type necrotizing and crescentic glomerulonephritis. According to previous reports from all over the world, the etiology, prevalence, and prognosis of RPGN including ANCA-associated renal vasculitis varies among races and periods. To elucidate the clinical characteristics of Japanese RPGN patients, a registry derived from a questionnaire survey was established in 1999 and maintained until 2006. As a result, 1,772 cases were collected, analyzed, and reported previously. In this mini-review, we outline the characteristic clinical findings of Japanese patients (Asian) with ANCA-associated renal vasculitis, based on the registry data.

Original languageEnglish
Pages (from-to)646-649
Number of pages4
JournalClinical and Experimental Nephrology
Volume17
Issue number5
DOIs
Publication statusPublished - Oct 2013

Keywords

  • ANCA-associated renal vasculitis
  • Japan
  • Questionnaire survey
  • RPGN
  • Registry

ASJC Scopus subject areas

  • Physiology
  • Nephrology
  • Physiology (medical)

Fingerprint Dive into the research topics of 'Clinical findings on ANCA-associated renal vasculitis from the Japan RPGN registry obtained via a questionnaire survey'. Together they form a unique fingerprint.

  • Cite this