Clinical findings on ANCA-associated renal vasculitis from the Japan RPGN registry obtained via a questionnaire survey

Kunihiro Yamagata, Joichi Usui, Hitoshi Sugiyama, Kosaku Nitta, Takashi Wada, Eri Muso, Yoshihiro Arimura, Akio Koyama, Hirofumi Makino, Seiichi Matsuo

Research output: Contribution to journalArticle

5 Citations (Scopus)

Abstract

Renal involvement with significant organ damage is common in anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV). As a result, it is independently referred to ANCA-associated renal vasculitis. Clinically, ANCA-associated renal vasculitis is characterized by rapidly progressive glomerulonephritis. Pathologically, it is defined by pauci-immune type necrotizing and crescentic glomerulonephritis. According to previous reports from all over the world, the etiology, prevalence, and prognosis of RPGN including ANCA-associated renal vasculitis varies among races and periods. To elucidate the clinical characteristics of Japanese RPGN patients, a registry derived from a questionnaire survey was established in 1999 and maintained until 2006. As a result, 1,772 cases were collected, analyzed, and reported previously. In this mini-review, we outline the characteristic clinical findings of Japanese patients (Asian) with ANCA-associated renal vasculitis, based on the registry data.

Original languageEnglish
Pages (from-to)646-649
Number of pages4
JournalClinical and Experimental Nephrology
Volume17
Issue number5
DOIs
Publication statusPublished - Oct 2013

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Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis
Registries
Japan
Kidney
Glomerulonephritis
Surveys and Questionnaires

Keywords

  • ANCA-associated renal vasculitis
  • Japan
  • Questionnaire survey
  • Registry
  • RPGN

ASJC Scopus subject areas

  • Nephrology
  • Physiology
  • Physiology (medical)

Cite this

Clinical findings on ANCA-associated renal vasculitis from the Japan RPGN registry obtained via a questionnaire survey. / Yamagata, Kunihiro; Usui, Joichi; Sugiyama, Hitoshi; Nitta, Kosaku; Wada, Takashi; Muso, Eri; Arimura, Yoshihiro; Koyama, Akio; Makino, Hirofumi; Matsuo, Seiichi.

In: Clinical and Experimental Nephrology, Vol. 17, No. 5, 10.2013, p. 646-649.

Research output: Contribution to journalArticle

Yamagata, Kunihiro ; Usui, Joichi ; Sugiyama, Hitoshi ; Nitta, Kosaku ; Wada, Takashi ; Muso, Eri ; Arimura, Yoshihiro ; Koyama, Akio ; Makino, Hirofumi ; Matsuo, Seiichi. / Clinical findings on ANCA-associated renal vasculitis from the Japan RPGN registry obtained via a questionnaire survey. In: Clinical and Experimental Nephrology. 2013 ; Vol. 17, No. 5. pp. 646-649.
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AU - Nitta, Kosaku

AU - Wada, Takashi

AU - Muso, Eri

AU - Arimura, Yoshihiro

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AU - Matsuo, Seiichi

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