An Elderly Male with Primary Sjögren’s Syndrome Presenting Pleuritis as the Initial Manifestation

Primary Sjögren’s syndrome (SS) is an autoimmune disease that usually affects the exocrine glands in middle-aged women. Fifteen percent of SS patients experience severe systemic extraglandular complications, and pleuritis is one of the rare complications of SS. We report the case of an elderly Japanese man who initially presented with a prolonged fever and chest pain and was finally diagnosed with primary SS-associated pleuritis. Of the nine reported cases of primary SS that initially presented with pleuritis, up to six cases were elderly males. This case highlights the complication of pleuritis among elderly males with primary SS