A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome

Yoshio Kawakami, Noritaka Oyama, Kazuhiro Kishimoto, Keiji Yamazaki, Akiko Nishibu, Koichiro Nakamura, Satoshi Hoshi, Fumio Kaneko

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We report a 27-year-old Japanese woman with Turner syndrome who had generalized pustular psoriasis of the von Zumbusch type. She developed a febrile diffuse erythema and pustular eruption without any history of preceding psoriasis vulgaris or drug ingestion. Oral treatment with 3.2 mg/kg cyclosporin per day successfully resulted in rapid improvement, followed by a complete remission. To our knowledge, this is the first report describing the unusual coexistence of these two systemic disorders. We discuss a hormone imbalance that might have contributed to the predisposition to pustular psoriasis and difficulties in the management of the patent's treatment.

Original languageEnglish
Pages (from-to)16-20
Number of pages5
JournalJournal of Dermatology
Issue number1
Publication statusPublished - Jan 2004


  • Chromosomal abnormality
  • Cyclosporin
  • Psoriasis vulgaris
  • Von Zumbusch type

ASJC Scopus subject areas

  • Dermatology

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    Kawakami, Y., Oyama, N., Kishimoto, K., Yamazaki, K., Nishibu, A., Nakamura, K., Hoshi, S., & Kaneko, F. (2004). A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome. Journal of Dermatology, 31(1), 16-20. https://doi.org/10.1111/j.1346-8138.2004.tb00498.x