A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome

Yoshio Kawakami, Noritaka Oyama, Kazuhiro Kishimoto, Keiji Yamazaki, Akiko Nishibu, Koichiro Nakamura, Satoshi Hoshi, Fumio Kaneko

Research output: Contribution to journalArticle

8 Citations (Scopus)

Abstract

We report a 27-year-old Japanese woman with Turner syndrome who had generalized pustular psoriasis of the von Zumbusch type. She developed a febrile diffuse erythema and pustular eruption without any history of preceding psoriasis vulgaris or drug ingestion. Oral treatment with 3.2 mg/kg cyclosporin per day successfully resulted in rapid improvement, followed by a complete remission. To our knowledge, this is the first report describing the unusual coexistence of these two systemic disorders. We discuss a hormone imbalance that might have contributed to the predisposition to pustular psoriasis and difficulties in the management of the patent's treatment.

Original languageEnglish
Pages (from-to)16-20
Number of pages5
JournalJournal of Dermatology
Volume31
Issue number1
DOIs
Publication statusPublished - Jan 1 2004
Externally publishedYes

Fingerprint

Turner Syndrome
Psoriasis
Patents
Erythema
Cyclosporine
Fever
Eating
Hormones
Therapeutics
Pharmaceutical Preparations

Keywords

  • Chromosomal abnormality
  • Cyclosporin
  • Psoriasis vulgaris
  • Von Zumbusch type

ASJC Scopus subject areas

  • Dermatology

Cite this

Kawakami, Y., Oyama, N., Kishimoto, K., Yamazaki, K., Nishibu, A., Nakamura, K., ... Kaneko, F. (2004). A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome. Journal of Dermatology, 31(1), 16-20. https://doi.org/10.1111/j.1346-8138.2004.tb00498.x

A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome. / Kawakami, Yoshio; Oyama, Noritaka; Kishimoto, Kazuhiro; Yamazaki, Keiji; Nishibu, Akiko; Nakamura, Koichiro; Hoshi, Satoshi; Kaneko, Fumio.

In: Journal of Dermatology, Vol. 31, No. 1, 01.01.2004, p. 16-20.

Research output: Contribution to journalArticle

Kawakami, Y, Oyama, N, Kishimoto, K, Yamazaki, K, Nishibu, A, Nakamura, K, Hoshi, S & Kaneko, F 2004, 'A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome', Journal of Dermatology, vol. 31, no. 1, pp. 16-20. https://doi.org/10.1111/j.1346-8138.2004.tb00498.x
Kawakami Y, Oyama N, Kishimoto K, Yamazaki K, Nishibu A, Nakamura K et al. A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome. Journal of Dermatology. 2004 Jan 1;31(1):16-20. https://doi.org/10.1111/j.1346-8138.2004.tb00498.x
Kawakami, Yoshio ; Oyama, Noritaka ; Kishimoto, Kazuhiro ; Yamazaki, Keiji ; Nishibu, Akiko ; Nakamura, Koichiro ; Hoshi, Satoshi ; Kaneko, Fumio. / A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome. In: Journal of Dermatology. 2004 ; Vol. 31, No. 1. pp. 16-20.
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